3-Methyl-2-oxobutanoic acid 是大肠杆菌中泛酸的前体。它是由支链氨基酸的不完全分解产生的一种异常代谢物。

alpha-Ketoisovaleric acid is an abnormal metabolite that arises from the incomplete breakdown of branched-chain amino acids. alpha-Ketoisovaleric acid is a neurotoxin, an acidogen, and a metabotoxin. A neurotoxin causes damage to nerve cells and nerve tissues. alpha-Ketoisovaleric acid is a keto-acid, which is a subclass of organic acids. Abnormally high levels of organic acids in the blood (organic acidemia), urine (organic aciduria), the brain, and other tissues lead to general metabolic acidosis.

759-05-7

C5H8O3

116.116

3-甲基-2-氧丁酸;2-Oxoisovaleric acid;alpha-Ketoisovaleric acid;3-Methyl-2-oxobutanoic acid

DMSO:10 mM
Powder: -20°C for 3 years
In solvent: -80°C for 2 years